CONGENITAL LOBAR EMPHYSEMA DEVELOPING MASSIVE HEMOPTYSIS IN ADULTHOOD TREATED BY THORACOSCOPIC LOBECTOMY

Objectives: Congenital lobar emphysema (CLE) arises mainly from intrinsic anomalies involving abnormal airway branching, usually with a defect in cartilage formation, resulting in progressive hyperinflation of the emphysematous lobe, compression of remaining lung parenchyma, and displacement of mediastinal structures. CLE is usually diagnosed within days of birth, and almost all cases are identified by six months of age. Very rarely an adolescent or adult CLE patient develops persistent cough, dyspnea or recurrent pulmonary infections requiring resection via lobectomy . Herein we present a case of a healthy adult with known CLE who presented with serious hemoptysis and was managed successfully by thoracoscopic lobectomy.

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